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DeCS
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Descriptor English:
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Idiopathic Pulmonary Fibrosis
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Descriptor Spanish:
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Fibrosis Pulmonar Idiopática
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Descriptor Portuguese:
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Fibrose Pulmonar Idiopática
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Synonyms English:
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Cryptogenic Fibrosing Alveolitides
Cryptogenic Fibrosing Alveolitis
Dysplasia, Fibrocystic Pulmonary
Familial Idiopathic Pulmonary Fibrosis
Fibrocystic Pulmonary Dysplasia
Fibrocystic Pulmonary Dysplasias
Fibrosing Alveolitides, Cryptogenic
Fibrosing Alveolitis, Cryptogenic
Idiopathic Fibrosing Alveolitis, Chronic Form
Idiopathic Pulmonary Fibroses
Idiopathic Pulmonary Fibrosis, Familial
Interstitial Pneumonia, Usual
Interstitial Pneumonitis, Usual
Pneumonitides, Usual Interstitial
Pneumonitis, Usual Interstitial
Pulmonary Dysplasia, Fibrocystic
Pulmonary Fibroses, Idiopathic
Pulmonary Fibrosis, Idiopathic
Usual Interstitial Pneumonia
Usual Interstitial Pneumonias
Usual Interstitial Pneumonitides
Usual Interstitial Pneumonitis
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Tree Number:
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C08.381.765.500
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Definition English:
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A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change. |
Indexing Annotation English:
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PULMONARY FIBROSIS is also available
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History Note English:
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2009
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Allowable Qualifiers English:
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Record Number:
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53083
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Unique Identifier:
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D054990
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Occurrence in VHL:
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Similar:
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DeCS
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