1 / 1
|
DeCS
|
|
|
Descriptor English:
|
|
Hyperostosis, Cortical, Congenital
|
Descriptor Spanish:
|
|
Hiperostosis Cortical Congénita
|
Descriptor Portuguese:
|
|
Hiperostose Cortical Congênita
|
Synonyms English:
|
|
Caffey De Toni Silvermann Syndrome
Caffey Disease
Caffey's Disease, Familial
Caffey-De Toni-Silvermann Syndrome
Congenital Cortical Hyperostoses
Congenital Cortical Hyperostosis
Congenital Hyperostoses, Cortical
Congenital Hyperostosis, Cortical
Cortical Congenital Hyperostoses
Cortical Congenital Hyperostosis
Cortical Hyperostoses, Congenital
Cortical Hyperostoses, Infantile
Cortical Hyperostosis, Congenital
Cortical Hyperostosis, Infantile
Disease, Caffey
Disease, Familial Caffey's
Familial Caffey Disease
Familial Caffey's Disease
Familial Caffeys Disease
Familial Infantile Cortical Hyperostosis
Hyperostoses, Congenital Cortical
Hyperostoses, Cortical Congenital
Hyperostoses, Infantile Cortical
Hyperostosis, Congenital Cortical
Hyperostosis, Cortical Congenital
Hyperostosis, Infantile Cortical
Infantile Cortical Hyperostoses
Infantile Cortical Hyperostosis
Syndrome, Caffey-De Toni-Silvermann
|
Tree Number:
|
|
C05.116.099.708.479
C05.116.540.400
C16.614.465
|
Definition English:
|
|
A disease of young infants characterized by soft tissue swellings over the affected bones, fever, and irritability, and marked by periods of remission and exacerbation. (Dorland, 27th ed) |
Indexing Annotation English:
|
|
cortical refers to cortex of bone; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
|
History Note English:
|
|
91; was HYPEROSTOSIS, CORTICAL CONGENITAL 1964-90
|
Allowable Qualifiers English:
|
|
|
Record Number:
|
|
29270
|
Unique Identifier:
|
|
D006958
|
Occurrence in VHL:
|
|
|
Similar:
|
|
DeCS
|
|