Search on: MFN=59279 
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Descriptor English:   Hamman-Rich Syndrome 
Descriptor Spanish:   Síndrome Hamman-Rich 
Descriptor Portuguese:   Síndrome de Hamman-Rich 
Synonyms English:   Acute Interstitial Pneumonia
Acute Interstitial Pneumonias
Acute Interstitial Pneumonitides
Acute Interstitial Pneumonitis
Hamman Rich Disease
Hamman Rich Syndrome
Hamman-Rich Disease
Hamman-Rich Diseases
Interstitial Pneumonia, Acute
Interstitial Pneumonitis, Acute
Pneumonia, Acute Interstitial
Pneumonitis, Acute Interstitial  
Tree Number:   C08.381.765.500.500
Definition English:   Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages. 
History Note English:   2020; for HAMMAN-RICH SYNDROME use PULMONARY FIBROSIS 1984-2019; for HAMMAN-RICH SYNDROME use IDIOPATHIC PULMONARY FIBROSIS 2010-2019 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   59279 
Unique Identifier:   D000080203 

Occurrence in VHL:
 

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