|
1 / 1
|
DeCS
|
|
 |
|
Descriptor English:
|
|
Subacute Sclerosing Panencephalitis
|
|
Descriptor Spanish:
|
|
Panencefalitis Esclerosante Subaguda
|
|
Descriptor Portuguese:
|
|
Panencefalite Esclerosante Subaguda
|
|
Synonyms English:
|
|
Encephalitis, Inclusion Body, Measles
Inclusion Body Encephalitis, Measles
Leukoencephalitides, Subacute Sclerosing
Leukoencephalitis, Subacute Sclerosing
Leukoencephalitis, Van Bogaert
Leukoencephalitis, Van Bogaert's
Leukoencephalitis, Van Bogaerts
Measles Inclusion Body Encephalitis
Panencephalitides, Subacute Sclerosing
Panencephalitis, Subacute Sclerosing
SSPE
Sclerosing Leukoencephalitides, Subacute
Sclerosing Leukoencephalitis, Subacute
Sclerosing Panencephalitides, Subacute
Sclerosing Panencephalitis, Subacute
Subacute Sclerosing Leukoencephalitides
Subacute Sclerosing Leukoencephalitis
Subacute Sclerosing Panencephalitides
Van Bogaert Leukoencephalitis
Van Bogaert's Leukoencephalitis
Van Bogaerts Leukoencephalitis
|
|
Tree Number:
|
|
C01.207.245.340.600
C01.207.399.750.600
C01.925.182.525.600
C01.925.782.580.600.500.500.800
C01.925.839.862
C10.228.140.430.520.750.600
C10.228.228.245.340.600
C10.228.228.399.750.600
|
|
Definition English:
|
|
A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8) |
|
History Note English:
|
|
71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70
|
|
Allowable Qualifiers English:
|
|
|
|
Record Number:
|
|
13732
|
|
Unique Identifier:
|
|
D013344
|
Occurrence in VHL:
|
|
|
Similar:
|
|
DeCS
|
|