Search on: RETINOBLASTOMA 
Descriptors Found: 1
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Descriptor English:   Retinoblastoma 
Descriptor Spanish:   Retinoblastoma 
Descriptor Portuguese:   Retinoblastoma 
Synonyms English:   Cancer, Retinoblastoma Eye
Cancers, Retinoblastoma Eye
Eye Cancer, Retinoblastoma
Eye Cancers, Retinoblastoma
Familial Retinoblastoma
Familial Retinoblastomas
Glioblastoma, Retinal
Glioblastomas, Retinal
Glioma, Retinal
Gliomas, Retinal
Hereditary Retinoblastoma
Hereditary Retinoblastomas
Neuroblastoma, Retinal
Neuroblastomas, Retinal
Retinal Glioblastoma
Retinal Glioblastomas
Retinal Glioma
Retinal Gliomas
Retinal Neuroblastoma
Retinal Neuroblastomas
Retinoblastoma Eye Cancer
Retinoblastoma Eye Cancers
Retinoblastoma, Familial
Retinoblastoma, Hereditary
Retinoblastoma, Sporadic
Retinoblastomas
Retinoblastomas, Familial
Retinoblastomas, Hereditary
Retinoblastomas, Sporadic
Sporadic Retinoblastoma
Sporadic Retinoblastomas  
Tree Number:   C04.557.465.625.600.725
C04.557.470.670.725
C04.557.580.625.600.725
C04.588.364.818.760
C11.270.862
C11.319.475.760
C11.768.717.760
Definition English:   A malignant tumor arising from the nuclear layer of the retina that is the most common primary tumor of the eye in children. The tumor tends to occur in early childhood or infancy and may be present at birth. The majority are sporadic, but the condition may be transmitted as an autosomal dominant trait. Histologic features include dense cellularity, small round polygonal cells, and areas of calcification and necrosis. An abnormal pupil reflex (leukokoria); NYSTAGMUS, PATHOLOGIC; STRABISMUS; and visual loss represent common clinical characteristics of this condition. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2104) 
Indexing Annotation English:   coordinate IM with RETINAL NEOPLASMS (IM); /genetics: consider also GENES, RETINOBLASTOMA
See Related English:   Genes, Retinoblastoma
 
Allowable Qualifiers English:  
BS blood supply BL blood
CF cerebrospinal fluid CI chemically induced
CH chemistry CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SC secondary SU surgery
TH therapy UL ultrastructure
UR urine VE veterinary
VI virology  
Record Number:   12591 
Unique Identifier:   D012175 

Occurrence in VHL:
 

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