Search on: PARAHEMOPHILIA 
Descriptors Found: 1
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Descriptor English:   Factor V Deficiency 
Descriptor Spanish:   Deficiencia del Factor V 
Descriptor Portuguese:   Deficiência do Fator V 
Synonyms English:   Deficiencies, Factor 5
Deficiencies, Factor Five
Deficiencies, Factor V
Deficiencies, Labile Factor
Deficiency, Factor 5
Deficiency, Factor Five
Deficiency, Factor V
Deficiency, Labile Factor
Disease, Owren
Disease, Owren's
Factor 5 Deficiencies
Factor 5 Deficiency
Factor Five Deficiencies
Factor Five Deficiency
Factor V Deficiencies
Labile Factor Deficiencies
Labile Factor Deficiency
Owren Disease
Owren Parahemophilia
Owren's Disease
Owrens Disease
Parahemophilia
Parahemophilia, Owren
Parahemophilias  
Tree Number:   C15.378.100.100.300
C15.378.100.141.300
C15.378.463.300
C16.320.099.300
Definition English:   A deficiency of blood coagulation factor V (known as proaccelerin or accelerator globulin or labile factor) leading to a rare hemorrhagic tendency known as Owren's disease or parahemophilia. It varies greatly in severity. Factor V deficiency is an autosomal recessive trait. (Dorland, 27th ed) 
Indexing Annotation English:   a blood coag disord
History Note English:   73(64); was see under HYPOPROTHROMBINEMIAS 1963-72 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   5266 
Unique Identifier:   D005166 

Occurrence in VHL:
 

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DeCS