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DeCS
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Descriptor English:
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Neurofibroma, Plexiform
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Descriptor Spanish:
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Neurofibroma Plexiforme
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Descriptor Portuguese:
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Neurofibroma Plexiforme
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Synonyms English:
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Elephantiasis Neuromatoses
Elephantiasis Neuromatosis
Neurofibromas, Plexiform
Neuroma, Plexiform
Neuromas, Plexiform
Pachydermatocele
Pachydermatoceles
Plexiform Neurofibroma
Plexiform Neurofibromas
Plexiform Neuroma
Plexiform Neuromas
Tumor Royale
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Tree Number:
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C04.557.580.600.580.585
C10.551.775.500.750.500
C10.668.829.725.500.600.500
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Definition English:
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A type of neurofibroma manifesting as a diffuse overgrowth of subcutaneous tissue, usually involving the face, scalp, neck, and chest but occasionally occurring in the abdomen or pelvis. The tumors tend to progress, and may extend along nerve roots to eventually involve the spinal roots and spinal cord. This process is almost always a manifestation of NEUROFIBROMATOSIS 1. (From Adams et al., Principles of Neurology, 6th ed, p1016; J Pediatr 1997 Nov;131(5):678-82) |
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Indexing Annotation English:
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coord IM with precoord organ/neopl term (IM)
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History Note English:
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94
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Allowable Qualifiers English:
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Record Number:
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31254
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Unique Identifier:
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D018318
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Occurrence in VHL:
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Similar:
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DeCS
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