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IPSID
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DeCS
Descriptor
English
:
Immunoproliferative Small Intestinal Disease
Descriptor
Spanish
:
Enfermedad Inmunoproliferativa del Intestino Delgado
Descriptor
Portuguese
:
Doença Imunoproliferativa do Intestino Delgado
Synonyms
English
:
Disease, alpha-Chain
Diseases, alpha-Chain
Heavy Chain Disease, IgA Type
IPSID
Lymphoma, Mediterranean
Mediterranean Lymphoma
alpha Chain Disease
alpha-Chain Disease
alpha-Chain Diseases
Tree Number:
C04.557.386.390
C06.301.371.411.512
C06.405.249.411.512
C06.405.469.491.505
C15.378.147.780.490.512
C15.604.515.435.512
C20.683.515.512
C20.683.780.490.512
Definition
English
:
A condition that is caused by
HYPERPLASIA
of
LYMPHOCYTES
in the small
intestine
(
INTESTINE
, SMALL) and the mesenteric
LYMPH NODES
. These
lymphocytes
produce an anomalous alpha heavy chain protein. Generally, these IPSID
patients
have either concurrent
LYMPHOMA
or develop
lymphoma
within a few years. The
disease
was first described in the
Mediterranean region
and is characterized by malabsorption;
WEIGHT LOSS
;
DIARRHEA
; and
STEATORRHEA.
History Note
English
:
87
Allowable Qualifiers
English
:
BL
blood
CF
cerebrospinal fluid
CI
chemically induced
CL
classification
CO
complications
CN
congenital
DI
diagnosis
DG
diagnostic imaging
DH
diet therapy
DT
drug therapy
EC
economics
EM
embryology
EN
enzymology
EP
epidemiology
EH
ethnology
ET
etiology
GE
genetics
HI
history
IM
immunology
ME
metabolism
MI
microbiology
MO
mortality
NU
nursing
PS
parasitology
PA
pathology
PP
physiopathology
PC
prevention & control
PX
psychology
RT
radiotherapy
RH
rehabilitation
SU
surgery
TH
therapy
UR
urine
VE
veterinary
VI
virology
Record Number:
19205
Unique Identifier:
D007161
Occurrence in VHL
:
Similar:
DeCS