Search on: GLUCAGONOMA 
Descriptors Found: 1
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Descriptor English:   Glucagonoma 
Descriptor Spanish:   Glucagonoma 
Descriptor Portuguese:   Glucagonoma 
Synonyms English:   Adenoma, alpha Cell
Adenoma, alpha-Cell
Adenomas, alpha-Cell
Glucagonoma Syndrome
Glucagonoma Syndromes
Glucagonomas
Syndrome, Glucagonoma
Syndromes, Glucagonoma
Tumor, alpha-Cell
Tumors, alpha-Cell
alpha Cell Tumor
alpha-Cell Adenoma
alpha-Cell Adenomas
alpha-Cell Tumor
alpha-Cell Tumors  
Tree Number:   C04.557.470.200.025.290.750
C04.588.274.761.500.249
C04.588.322.475.500.249
C06.301.761.500.249
C06.689.667.500.249
C19.344.421.500.249
Definition English:   An almost always malignant GLUCAGON-secreting tumor derived from the PANCREATIC ALPHA CELLS. It is characterized by a distinctive migratory ERYTHEMA; WEIGHT LOSS; STOMATITIS; GLOSSITIS; DIABETES MELLITUS; hypoaminoacidemia; and normochromic normocytic ANEMIA. 
Indexing Annotation English:   coordinate IM with PANCREATIC NEOPLASMS (IM); for glucagonoma syndrome, coordinate also with NECROLYTIC MIGRATORY ERYTHEMA
See Related English:   Necrolytic Migratory Erythema
 
History Note English:   91(82); was see under ISLET CELL TUMOR 1982-90; was see ISLET CELL TUMOR 1981 
Allowable Qualifiers English:  
BS blood supply BL blood
CF cerebrospinal fluid CI chemically induced
CH chemistry CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SC secondary SU surgery
TH therapy UL ultrastructure
UR urine VE veterinary
VI virology  
Record Number:   6079 
Unique Identifier:   D005935 

Occurrence in VHL:
 

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