Descriptors Found: 1
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Descriptor English:   Shy-Drager Syndrome 
Descriptor Spanish:   Síndrome de Shy-Drager 
Descriptor Portuguese:   Síndrome de Shy-Drager 
Synonyms English:   Autonomic Failure, Progressive
Autonomic Failures, Progressive
Dysautonomia Orthostatic Hypotension Syndrome
Dysautonomia-Orthostatic Hypotension Syndrome
Dysautonomia-Orthostatic Hypotension Syndromes
Dysautonomic Orthostatic Hypotension
Dysautonomic Orthostatic Hypotensions
Failure, Progressive Autonomic
Failures, Progressive Autonomic
Hypotension Syndrome, Dysautonomia-Orthostatic
Hypotension Syndromes, Dysautonomia-Orthostatic
Hypotension, Dysautonomic Orthostatic
Hypotensions, Dysautonomic Orthostatic
Idiopathic Orthostatic Hypotension, Shy Drager Type
Idiopathic Orthostatic Hypotension, Shy-Drager Type
Orthostatic Hypotension, Dysautonomic
Orthostatic Hypotensions, Dysautonomic
Progressive Autonomic Failure
Progressive Autonomic Failures
Shy Drager Syndrome
Syndrome, Dysautonomia Orthostatic Hypotension
Syndrome, Dysautonomia-Orthostatic Hypotension
Syndrome, Shy-Drager
Syndromes, Dysautonomia-Orthostatic Hypotension  
Tree Number:   C10.177.575.550.750
Definition English:   A progressive neurodegenerative condition of the central and autonomic nervous systems characterized by atrophy of the preganglionic lateral horn neurons of the thoracic spinal cord. This disease is generally considered a clinical variant of MULTIPLE SYSTEM ATROPHY. Affected individuals present in the fifth or sixth decade with ORTHOSTASIS and bladder dysfunction; and later develop FECAL INCONTINENCE; anhidrosis; ATAXIA; IMPOTENCE; and alterations of tone suggestive of basal ganglia dysfunction. (From Adams et al., Principles of Neurology, 6th ed, p536) 
See Related English:   Multiple System Atrophy
History Note English:   1991(1981) 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   13172 
Unique Identifier:   D012791 

Occurrence in VHL: