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Descriptors Found: 1
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Descriptor English:   Fibromatosis, Aggressive 
Descriptor Spanish:   Fibromatosis Agresiva 
Descriptor Portuguese:   Fibromatose Agressiva 
Synonyms English:   Aggressive Fibromatoses
Aggressive Fibromatosis
Desmoid
Desmoids
Fibromatoses, Aggressive  
Tree Number:   C04.557.450.565.590.340.410
Definition English:   A childhood counterpart of abdominal or extra-abdominal desmoid tumors, characterized by firm subcutaneous nodules that grow rapidly in any part of the body but do not metastasize. The adult form of abdominal fibromatosis is FIBROMATOSIS, ABDOMINAL. (Stedman, 25th ed) 
Indexing Annotation English:   coordinate with precoordinated organ/neoplasm term if specified
History Note English:   94; DESMOID was see FIBROMA 1991-93 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   31469 
Unique Identifier:   D018222 

Occurrence in VHL:
 

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