|
1 / 1
|
DeCS
|
|
 |
|
Descriptor English:
|
|
Dermatomyositis
|
|
Descriptor Spanish:
|
|
Dermatomiositis
|
|
Descriptor Portuguese:
|
|
Dermatomiosite
|
|
Synonyms English:
|
|
Adult Type Dermatomyositis
Childhood Type Dermatomyositis
Dermatomyositis, Adult Type
Dermatomyositis, Childhood Type
Dermatomyositis, Juvenile
Dermatopolymyositis
Juvenile Dermatomyositis
Juvenile Myositis
Myositis, Juvenile
Polymyositis Dermatomyositis
Polymyositis-Dermatomyositis
|
|
Tree Number:
|
|
C05.651.594.819.500
C10.668.491.562.575.500
C17.300.250
C17.800.185
|
|
Definition English:
|
|
A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6) |
|
Indexing Annotation English:
|
|
coordinate with PARANEOPLASTIC SYNDROMES if pertinent
|
|
Allowable Qualifiers English:
|
|
|
|
Record Number:
|
|
3902
|
|
Unique Identifier:
|
|
D003882
|
Occurrence in VHL:
|
|
|
Similar:
|
|
DeCS
|
|