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Descriptor English:   Cryptogenic Organizing Pneumonia 
Descriptor Spanish:   Neumonía en Organización Criptogénica 
Descriptor Portuguese:   Pneumonia em Organização Criptogênica 
Synonyms English:   BOOP
Bronchiolitis Obliterans Organizing Pneumonia
Cryptogenic Organizing Pneumonias
Organizing Pneumonia, Cryptogenic
Organizing Pneumonias, Cryptogenic
Pneumonia, Cryptogenic Organizing
Pneumonias, Cryptogenic Organizing  
Tree Number:   C08.127.446.135.140.200
C08.381.483.487.249
C08.381.495.146.135.140.200
C08.381.765.500.750.249
Definition English:   An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts. 
Indexing Annotation English:   note entry term BRONCHIOLITIS OBLITERANS ORGANIZING PNEUMONIA: do not confuse with BRONCHIOLITIS OBLITERANS
History Note English:   2009 (1995) 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   32330 
Unique Identifier:   D018549 

Occurrence in VHL:
 

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