Descriptors Found: 1
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Descriptor English:   Multiple System Atrophy 
Descriptor Spanish:   Atrofia de Múltiples Sistemas 
Descriptor Portuguese:   Atrofia de Múltiplos Sistemas 
Synonyms English:   Atrophies, Multisystem
Atrophies, Multisystemic
Atrophy, Multiple System
Atrophy, Multisystem
Atrophy, Multisystemic
Multiple System Atrophies
Multiple System Atrophy Syndrome
Multisystem Atrophies
Multisystem Atrophy
Multisystemic Atrophies
Multisystemic Atrophy  
Tree Number:   C10.177.575.550
Definition English:   A syndrome complex composed of three conditions which represent clinical variants of the same disease process: STRIATONIGRAL DEGENERATION; SHY-DRAGER SYNDROME; and the sporadic form of OLIVOPONTOCEREBELLAR ATROPHIES. Clinical features include autonomic, cerebellar, and basal ganglia dysfunction. Pathologic examination reveals atrophy of the basal ganglia, cerebellum, pons, and medulla, with prominent loss of autonomic neurons in the brain stem and spinal cord. (From Adams et al., Principles of Neurology, 6th ed, p1076; Baillieres Clin Neurol 1997 Apr;6(1):187-204; Med Clin North Am 1999 Mar;83(2):381-92) 
Indexing Annotation English:   a specific neurodegenerative syndrome complex; not for atrophy in other systems
See Related English:   Olivopontocerebellar Atrophies
Shy-Drager Syndrome
History Note English:   1998 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   33352 
Unique Identifier:   D019578 

Occurrence in VHL: