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DeCS
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Descriptor English:
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Iduronidase
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Descriptor Spanish:
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Iduronidasa
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Descriptor Portuguese:
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Iduronidase
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Synonyms English:
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alpha L Idosiduronase
alpha L Iduronidase
alpha-L-Idosiduronase
alpha-L-Iduronidase
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Tree Number:
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D08.811.277.450.560
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Definition English:
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An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces Hurler's syndrome. EC 3.2.1.76. |
Indexing Annotation English:
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/defic: consider also MUCOPOLYSACCHARIDOSIS I
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See Related English:
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Mucopolysaccharidosis I
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History Note English:
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91(75); was see under GLYCOSIDE HYDROLASES 1975-90
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Allowable Qualifiers English:
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Record Number:
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7251
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Unique Identifier:
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D007068
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Occurrence in VHL:
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Similar:
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DeCS
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