1 / 1
|
DeCS
|
|
|
Descriptor English:
|
|
von Willebrand Diseases
|
Descriptor Spanish:
|
|
Enfermedades de von Willebrand
|
Descriptor Portuguese:
|
|
Doenças de von Willebrand
|
Synonyms English:
|
|
Angiohemophilia
Angiohemophilias
Disorder, Von Willebrand
Hemophilia, Vascular
Pseudohemophilia, Vascular
Pseudohemophilias, Vascular
Vascular Hemophilia
Vascular Hemophilias
Vascular Pseudohemophilia
Vascular Pseudohemophilias
Von Willebrand Disorder
Von Willebrand's Factor Deficiency
von Willebrand Disease
von Willebrand Disease, Recessive Form
von Willebrand's Disease
von Willebrand's Diseases
|
Tree Number:
|
|
C15.378.100.100.900
C15.378.100.141.900
C15.378.140.900
C15.378.463.920
C16.320.099.920
|
Definition English:
|
|
Group of hemorrhagic disorders in which the VON WILLEBRAND FACTOR is either quantitatively or qualitatively abnormal. They are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. Symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor VIII, and impaired platelet adhesion. |
Indexing Annotation English:
|
|
note specific types of Von Willebrand Disease are available
|
History Note English:
|
|
2010(1963)
|
Allowable Qualifiers English:
|
|
|
Record Number:
|
|
15243
|
Unique Identifier:
|
|
D014842
|
Occurrence in VHL:
|
|
|
Similar:
|
|
DeCS
|