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DeCS
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Descriptor English:
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Pulmonary Subvalvular Stenosis
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Descriptor Spanish:
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Estenosis Subvalvular Pulmonar
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Descriptor Portuguese:
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Estenose Subvalvar Pulmonar
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Synonyms English:
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Conus, Obstructive Subaortic
Infundibular Stenoses, Pulmonary
Infundibular Stenosis, Pulmonary
Obstructive Subaortic Conus
Pulmonary Infundibular Stenoses
Pulmonary Infundibular Stenosis
Pulmonary Stenoses, Subvalvular
Pulmonary Stenosis, Subvalvular
Pulmonary Subvalvular Stenoses
Stenoses, Pulmonary Infundibular
Stenoses, Pulmonary Subvalvular
Stenoses, Subvalvular Pulmonary
Stenosis, Pulmonary Infundibular
Stenosis, Pulmonary Subvalvular
Stenosis, Subvalvular Pulmonary
Subaortic Conus, Obstructive
Subvalvular Pulmonary Stenoses
Subvalvular Pulmonary Stenosis
Subvalvular Stenoses, Pulmonary
Subvalvular Stenosis, Pulmonary
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Tree Number:
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C14.280.484.716.762
C14.280.955.750.762
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Definition English:
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Narrowing below the PULMONARY VALVE or well below it in the infundibuluar chamber where the pulmonary artery originates, usually caused by a defective VENTRICULAR SEPTUM or presence of fibrous tissues. It is characterized by restricted blood outflow from the RIGHT VENTRICLE into the PULMONARY ARTERY, exertional fatigue, DYSPNEA, and chest discomfort. |
Indexing Annotation English:
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do not confuse with PULMONARY VALVE STENOSIS; if secondary to idiopathic hypertrophic subaortic stenosis, coordinate with CARDIOMYOPATHY, HYPERTROPHIC; DF: PULM SUBVALV STENOSIS
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History Note English:
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91(75); was see under CARDIOMYOPATHY, HYPERTROPHIC 1986-90; was see under IDIOPATHIC HYPERTROPHIC SUBVALVULAR STENOSIS 1967-85
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Allowable Qualifiers English:
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Record Number:
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12099
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Unique Identifier:
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D011662
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Occurrence in VHL:
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Similar:
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DeCS
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